Peri-operative management of a neonate with tracheo-oesophageal fistula and anorectal malformation: Survival of the fittest
نویسندگان
چکیده
Oesophageal atresia (OA) with tracheo‐oesophageal fistula (TOF) is a rare congenital anomaly usually seen in association with the VACTERL spectrum of disorders in neonates.[1] Management of these groups of anomalies is generally an early surgical intervention in most cases. Majority of neonates are managed with a palliative procedure until fit for a definitive surgery.[2] Isolated case reports have been published about management of multiple defects.[3,4] We describe a case of a neonate with a high anorectal malformation (ARM) along with TOF who was managed surgically in a single setting for both defects. The pathophysiology of TOF gets further accentuated in a setting of ARM as there is absolutely no way to decompress the bowel, either from above or below. This calls for an urgent intervention in the form of a colostomy/gastrostomy or definitive repair, given further compromise of the already susceptible lungs.
منابع مشابه
Tracheo-Oesophageal Fistula with Anorectal Malformation and Colonic Agenesis: A Case Report
Esophageal atresia with Tracheoesophageal fistula (EA +TEF) is frequently associated with other congenital anomalies. The commonly associated systems are cardiovascular and gastrointestinal, including anorectal malformations. The associated anomalies adversely affect the outcome of the patient. Based on this association Waterson has given a criteria for risk stratification and survival of neona...
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Oesophageal atresia and/or tracheo-oesophageal fistula are relatively common malformations occurring in approximately 1 in 3500 births. In around half of the cases (syndromic oesophageal atresia), there are associated anomalies, with cardiac malformations being the most common. In the remainder (non-syndromic cases), oesophageal atresia/tracheo-oesophageal fistula occur in isolation. Data from ...
متن کاملOesophageal atresia, tracheo-oesophageal fistula and the VACTERL association: review of genetics and epidemiology. Charles Shaw-Smith Department of Medical Genetics, Addenbrooke’s Hospital, Cambridge CB2 2QQ, Address for correspondence:
Oesophageal atresia and/or tracheo-oesophageal fistula are common malformations occurring in approximately 1 in 3500 births. In around half of cases (syndromic oesophageal atresia), there are other associated anomalies, with cardiac malformations being the most common. These may occur as part of the VACTERL association (OMIM 192350). In the remainder of cases, oesophageal atresia/tracheo-oesoph...
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